Cochlear implant in a patient with neurofibromatosis type 2 undergoing radiotherapy.
نویسندگان
چکیده
eurofibromatosis type 2 (NF2) is a rare disease, characerized by a mutation in the long arm of chromosome 2 that leads to the development of bilateral vestibular chwannomas (VS) in approximately 90% of patients with this yndrome.1--4 The control of tumor growth and hearing preservation are he cornerstones of its treatment, which can be carried out y surgery or radiotherapy, considering the size of the lesion nd the presence of functional hearing. The possibilities of hearing rehabilitation range from the daptation of conventional hearing aids (HA) to auditory
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Hearing optimisation in neurofibromatosis type 2: A systematic review.
BACKGROUND It is common for patients with neurofibromatosis type 2 to develop bilateral profound hearing loss hearing loss, and this is one of the main determinants of quality of life in this patient group. OBJECTIVES The aim of this systematic review was to review the current literature regarding hearing outcomes of treatments for vestibular schwannomas in neurofibromatosis type 2 including ...
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ورودعنوان ژورنال:
- Brazilian journal of otorhinolaryngology
دوره 82 2 شماره
صفحات -
تاریخ انتشار 2016